Concentration Details

Metabolite
HMDB0061189 (3-Hydroxyisovalerylcarnitine)
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
3.56 uM
Age
Children (1-13 years old)
Sex
Female
Condition
multiple carboxylase deficiency
References
    1. Maeda Y, Ito T, Ohmi H, Yokoi K, Nakajima Y, Ueta A, Kurono Y, Togari H, Sugiyama N: Determination of 3-hydroxyisovalerylcarnitine and other acylcarnitine levels using liquid chromatography-tandem mass spectrometry in serum and urine of a patient with multiple carboxylase deficiency. J Chromatogr B Analyt Technol Biomed Life Sci. 2008 Jul 15;870(2):154-9. Epub 2007 Dec 4. [PubMed:18088573 ]