Concentration Details

Metabolite
HMDB0000123 (Glycine)
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
290 uM
Age
Children (1 - 13 years old)
Sex
Female
Condition
3-Methylcrotonyl-CoA Carboxylase Deficiency
References
    1. Rutledge SL, Berry GT, Stanley CA, van Hove JL, Millington D: Glycine and L-carnitine therapy in 3-methylcrotonyl-CoA carboxylase deficiency. J Inherit Metab Dis. 1995;18(3):299-305. [PubMed:7474896 ]