Concentration Details

Metabolite
HMDB0000359 (3alpha,7alpha-Dihydroxycoprostanic acid)
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
0.403 - 0.842 uM
Age
Children (1 - 13 years old)
Sex
Male
Condition
Classicle Refsum's disease
References
    1. Poll-The BT, Saudubray JM, Ogier H, Schutgens RB, Wanders RJ, Schrakamp G, van den Bosch H, Trijbels JM, Poulos A, Moser HW, et al.: Infantile Refsum's disease: biochemical findings suggesting multiple peroxisomal dysfunction. J Inherit Metab Dis. 1986;9(2):169-74. [PubMed:2427795 ]