Concentration Details

Metabolite
HMDB0200014 (CL(11:0/a-17:0/22:0/24:0))
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
>1 uM
Age
Infant (0-1 year old)
Sex
Not Specified
Condition
Long chain acyl-CoA dehydrogenase deficiency (LCAD)
References
    1. Liebig M, Schymik I, Mueller M, Wendel U, Mayatepek E, Ruiter J, Strauss AW, Wanders RJ, Spiekerkoetter U: Neonatal screening for very long-chain acyl-coA dehydrogenase deficiency: enzymatic and molecular evaluation of neonates with elevated C14:1-carnitine levels. Pediatrics. 2006 Sep;118(3):1065-9. doi: 10.1542/peds.2006-0666. [PubMed:16950999 ]