Concentration Details

Metabolite
HMDB0000716 (L-Pipecolic acid)
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
9.7 +/- 3.1 uM
Age
Adult (>18 years old)
Sex
Both
Condition
Zellweger syndrome
References
    1. Watkins PA, Chen WW, Harris CJ, Hoefler G, Hoefler S, Blake DC Jr, Balfe A, Kelley RI, Moser AB, Beard ME, et al.: Peroxisomal bifunctional enzyme deficiency. J Clin Invest. 1989 Mar;83(3):771-7. [PubMed:2921319 ]