Concentration Details

Metabolite
HMDB0000521 (5Z-Tetradecenoic acid)
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
215 +/- 174 uM
Age
Children (1-13 years old)
Sex
Both
Condition
Very long-chain acyl-CoA dehydrogenase deficiency (vLCAD)
References
    1. Divry P, Vianey-Saban C, Mathieu M: Determination of total fatty acids in plasma: cis-5-tetradecenoic acid (C14:1 omega-9) in the diagnosis of long-chain fatty acid oxidation defects. J Inherit Metab Dis. 1999 May;22(3):286-8. [PubMed:10384388 ]