Concentration Details

Metabolite
HMDB0000688 (Isovalerylcarnitine)
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
0.052 (0.022-0.068) uM
Age
Adult (>18 years old)
Sex
Both
Condition
Very long-chain acyl-CoA dehydrogenase deficiency (vLCAD)
References
    1. Costa CG, Struys EA, Bootsma A, ten Brink HJ, Dorland L, Tavares de Almeida I, Duran M, Jakobs C: Quantitative analysis of plasma acylcarnitines using gas chromatography chemical ionization mass fragmentography. J Lipid Res. 1997 Jan;38(1):173-82. [PubMed:9034211 ]