Concentration Details

Metabolite
HMDB0000754 (3-Hydroxyisovaleric acid)
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
88.0 (10.0-166.0) uM
Age
Children (1-13 years old)
Sex
Both
Condition
Biotinidase deficiency
References
    1. G.Frauendienst-Egger, Friedrich K. Trefz (2017). MetaGene: Metabolic & Genetic Information Center (MIC: http://www.metagene.de). METAGENE consortium.